肿瘤

汪飞　钱邦平　邱勇

Congenital scoliosis (CS) combined with the Sprengel’s deformity was a rare and complicated congenital deformity. Although the pathogenesis of this complicated deformity was still unclear, some existing studies revealed that Sprengel’s deformity occurred most frequently in congenital scoliosis with unilateral failure of vertebral segmentation in cervicothoracic or thoracic segments. According to the relationship between the congenital scoliosis and the Sprengel’s deformity, the complicated congenital deformity could be divided into 3 types: the elevated shoulder occurred on the convex side of the scoliosis, on the concave side of the scoliosis and CS combined with bilateral Sprengel’s deformity. A thorough physical examination and comprehensive using of three-dimensional computed tomography (CT) and magnetic resonance imaging (MRI) were very important for the assessment of this complicated deformity. The Sprengel’s deformity occurred on the convex side of upper thoracic congenital scoliosis usually required one-stage surgery to elevate scapula and correct the spinal deformity. The one-stage reduction of the elevated scapula was not necessarily needed when the Sprengel’s deformity occurred on the concave side of the scoliosis, because the elevated scapula could partially compensate the cosmetic deformity and minimize shoulder asymmetry.